{"id":943,"date":"2019-05-31T16:58:53","date_gmt":"2019-05-31T14:58:53","guid":{"rendered":"https:\/\/blog.ikosecm.it\/?p=943"},"modified":"2022-01-19T14:55:22","modified_gmt":"2022-01-19T13:55:22","slug":"la-distrofia-muscolare-di-duchenne","status":"publish","type":"post","link":"https:\/\/www.ikosecm.it\/ecm\/corsi-ecm\/la-distrofia-muscolare-di-duchenne\/","title":{"rendered":"La Distrofia Muscolare di Duchenne"},"content":{"rendered":"\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-1469jj-bd2f7276c2e4f24cba2f24a83367f627\">\n#top .av-special-heading.av-1469jj-bd2f7276c2e4f24cba2f24a83367f627{\nmargin:40px 0 50px 0;\npadding-bottom:10px;\n}\nbody .av-special-heading.av-1469jj-bd2f7276c2e4f24cba2f24a83367f627 .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-1469jj-bd2f7276c2e4f24cba2f24a83367f627 .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-1469jj-bd2f7276c2e4f24cba2f24a83367f627 av-special-heading-h2 blockquote modern-quote  avia-builder-el-0  el_before_av_one_full  avia-builder-el-first '><h2 class='av-special-heading-tag '  itemprop=\"headline\"  >Cos\u2018\u00e8, quando compare, che organi coinvolge e quale pu\u00f2 essere l\u2019approccio terapeutico?<\/h2><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4\">\n.flex_column.av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4 av_one_full  avia-builder-el-1  el_after_av_heading  el_before_av_heading  first flex_column_div av-zero-column-padding  '     ><p>\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-jwb5ix4d-5263dc0de01719ed849b85ccb4107b26\">\n#top .av-special-heading.av-jwb5ix4d-5263dc0de01719ed849b85ccb4107b26{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-jwb5ix4d-5263dc0de01719ed849b85ccb4107b26 .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-jwb5ix4d-5263dc0de01719ed849b85ccb4107b26 .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-jwb5ix4d-5263dc0de01719ed849b85ccb4107b26 av-special-heading-h4  avia-builder-el-2  el_before_av_textblock  avia-builder-el-first '><h4 class='av-special-heading-tag '  itemprop=\"headline\"  >Cosa si intende per distrofia muscolare?<\/h4><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div><br \/>\n<section  class='av_textblock_section av-jtaabdl7-515da227f3ed4c1f141e834a752c5dbc '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><p><!--more--><\/p>\n<div class=\"page\" title=\"Page 5\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 5\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<p>La distrofia muscolare \u00e8 una miopatia strutturale geneticamente determinata. \u00c8 altres\u00ec una definizione generica con la quale ci si riferisce a un gruppo piuttosto variegato di gravi patologie neuromuscolari.<\/p>\n<p>Parliamo di una malattia progressiva e degenerativa che colpisce il muscolo scheletrico e\/o il muscolo cardiaco.<\/p>\n<p>La\u201cfamiglia\u201d delle distrofie muscolari \u00e8 definibile come entit\u00e0 genetiche dovute a mutazioni in geni il cui difetto determina la perdita del corretto funzionamento del sistema del <strong>sarcolemma<\/strong>.<\/p>\n<p>La via finale comune consiste nella necrosi e nella degenerazione delle fibre muscolari scheletriche\/cardiache seguite da rigenerazione e sostituzione adiposa\/connettivale con i caratteristici cambiamenti \u201cdistrofici\u201d.<\/p>\n<\/div>\n<\/div>\n<\/div>\n<div class=\"page\" title=\"Page 6\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"page\" title=\"Page 6\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\"><\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div><\/section><br \/>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-1cmih3-09a5fd2d7f510bcdd4b4e3099902b29e\">\n#top .av-special-heading.av-1cmih3-09a5fd2d7f510bcdd4b4e3099902b29e{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-1cmih3-09a5fd2d7f510bcdd4b4e3099902b29e .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-1cmih3-09a5fd2d7f510bcdd4b4e3099902b29e .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-1cmih3-09a5fd2d7f510bcdd4b4e3099902b29e av-special-heading-h4  avia-builder-el-4  el_after_av_textblock  el_before_av_textblock '><h4 class='av-special-heading-tag '  itemprop=\"headline\"  >La distrofia muscolare di Duchenne<\/h4><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div><br \/>\n<section  class='av_textblock_section av-jtaabdl7-515da227f3ed4c1f141e834a752c5dbc '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><p><!--more--><\/p>\n<div class=\"page\" title=\"Page 5\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 5\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<p>Nello specifico, la <strong>distrofia muscolare di Duchenne<\/strong> rientra nella sottofamiglia delle <em>distrofinopatie<\/em>, ovvero malattie genetiche ereditate come un carattere mendeliano X-linked recessivo e sono causate da mutazioni nel gene della distrofina<b>.<\/b><\/p>\n<p>Possono essere affetti solo i maschi.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<ul>\n<li>Le femmine possono essere portatrici sane.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Le donne portatrici hanno un rischio del 50% di avere figli maschi malati ad ogni gravidanza.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>I maschi affetti hanno figlie portatrici sane e figli maschi sani.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>L\u2019ereditariet\u00e0 \u00e8 per il 70% di fonte materna. Questa percentuale comprende anche un 15% di mutazioni germinali.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Il restante 30% proviene da mutazioni ex-novo.<\/li>\n<\/ul>\n<\/div>\n<\/div>\n<\/div>\n<div class=\"page\" title=\"Page 6\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"page\" title=\"Page 6\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\"><\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div><\/section><br \/>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-jw0pkg1e-caa214345d7badf68510cc2fedfcc8d1\">\n.avia-image-container.av-jw0pkg1e-caa214345d7badf68510cc2fedfcc8d1 img.avia_image{\nbox-shadow:none;\n}\n.avia-image-container.av-jw0pkg1e-caa214345d7badf68510cc2fedfcc8d1 .av-image-caption-overlay-center{\ncolor:#ffffff;\n}\n<\/style>\n<div  class='avia-image-container av-jw0pkg1e-caa214345d7badf68510cc2fedfcc8d1 av-styling- avia-align-center  avia-builder-el-6  el_after_av_textblock  avia-builder-el-last '   itemprop=\"image\" itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/ImageObject\" ><div class=\"avia-image-container-inner\"><div class=\"avia-image-overlay-wrap\"><img decoding=\"async\" fetchpriority=\"high\" class='wp-image-966 avia-img-lazy-loading-not-966 avia_image ' src=\"https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/2.jpg\" alt='' title='sarcolemma'  height=\"559\" width=\"795\"  itemprop=\"thumbnailUrl\" srcset=\"https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/2.jpg 795w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/2-300x211.jpg 300w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/2-768x540.jpg 768w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/2-705x496.jpg 705w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/2-450x316.jpg 450w\" sizes=\"(max-width: 795px) 100vw, 795px\" \/><\/div><\/div><\/div><\/p><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-31dgf-d247fb43bc784c1b2af105c9da71b52b\">\n#top .av-special-heading.av-31dgf-d247fb43bc784c1b2af105c9da71b52b{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-31dgf-d247fb43bc784c1b2af105c9da71b52b .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-31dgf-d247fb43bc784c1b2af105c9da71b52b .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-31dgf-d247fb43bc784c1b2af105c9da71b52b av-special-heading-h4  avia-builder-el-7  el_after_av_one_full  el_before_av_one_full '><h4 class='av-special-heading-tag '  itemprop=\"headline\"  >Il quadro clinico <\/h4><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4\">\n.flex_column.av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4 av_one_full  avia-builder-el-8  el_after_av_heading  el_before_av_textblock  first flex_column_div av-zero-column-padding  '     ><section  class='av_textblock_section av-jtaabdl7-515da227f3ed4c1f141e834a752c5dbc '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><div class=\"page\" title=\"Page 5\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<p>Questa malattia all\u2019esordio presenta una sintomatologia con queste caratteristiche:<\/p>\n<ul>\n<li>Andatura anserina<\/li>\n<li>Frequenti cadute<\/li>\n<li>Difficolt\u00e0 a salire le scale<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Pseudoipertrofia del tricipite surale<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Deambulazione in punta di piedi<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<\/ul>\n<p>I primi sintomi sono generalmente rappresentati quindi da difficolt\u00e0 nel camminare.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Quest\u2019abilit\u00e0 tarda a comparire, oppure il bambino impara a camminare con un\u2019andatura impacciata, &#8220;anserina&#8221; (oscillante) a base allargata, in iperlordosi e con i piedi spinati, incontra progressive difficolt\u00e0 a salire le scale, corre a piccoli passi e cade frequentemente.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Sono generalmente evidenti le difficolt\u00e0 ad alzarsi da terra e dalla posizione seduta.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Spesso, nei primi stadi della malattia, il bambino lamenta dolore alle gambe, che compare improvvisamente e scompare in due o tre giorni, specie ai muscoli del polpaccio, particolarmente dopo attivit\u00e0 intensa.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Una volta conclamata invece il quadro clinico si modifica in questo modo:<\/p>\n<ul>\n<li>Esordio dopo i tre anni<\/li>\n<li>Ipertrofia dei cingoli con scapole alate<\/li>\n<li>Accentuazione della lordosi lombare<\/li>\n<li>Ipotonia<\/li>\n<li>Riduzione prossimale della forza muscolare<\/li>\n<li>Atrofia muscolare e retrazioni tendinee (tendine di Achille)<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Perdita della deambulazione autonoma<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<\/ul>\n<div class=\"page\" title=\"Page 6\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"page\" title=\"Page 6\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\"><\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div><\/section><br \/>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-jw0pkg1e-b749e4c100eb6ef80e461de2faa44c68\">\n.avia-image-container.av-jw0pkg1e-b749e4c100eb6ef80e461de2faa44c68 img.avia_image{\nbox-shadow:none;\n}\n.avia-image-container.av-jw0pkg1e-b749e4c100eb6ef80e461de2faa44c68 .av-image-caption-overlay-center{\ncolor:#ffffff;\n}\n<\/style>\n<div  class='avia-image-container av-jw0pkg1e-b749e4c100eb6ef80e461de2faa44c68 av-styling- avia-align-center  avia-builder-el-10  el_after_av_textblock  avia-builder-el-last '   itemprop=\"image\" itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/ImageObject\" ><div class=\"avia-image-container-inner\"><div class=\"avia-image-overlay-wrap\"><img decoding=\"async\" fetchpriority=\"high\" class='wp-image-950 avia-img-lazy-loading-not-950 avia_image ' src=\"https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/DMD_CAP_1-283x300.jpg\" alt='' title='andatura distrofia'  height=\"300\" width=\"283\"  itemprop=\"thumbnailUrl\" srcset=\"https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/DMD_CAP_1-283x300.jpg 283w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/DMD_CAP_1-450x477.jpg 450w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/DMD_CAP_1.jpg 604w\" sizes=\"(max-width: 283px) 100vw, 283px\" \/><\/div><\/div><\/div><\/p><\/div>\n<section  class='av_textblock_section av-jucse33e-b78725f91ac2803dba2f22cd03ab5675 '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><p><!--more--><\/p>\n<\/div><\/section>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-ju9svqe3-8cfd165acfd648d82f1c858e30ff1e0a\">\n#top .hr.hr-invisible.av-ju9svqe3-8cfd165acfd648d82f1c858e30ff1e0a{\nheight:30px;\n}\n<\/style>\n<div  class='hr av-ju9svqe3-8cfd165acfd648d82f1c858e30ff1e0a hr-invisible  avia-builder-el-12  el_after_av_textblock  el_before_av_heading '><span class='hr-inner '><span class=\"hr-inner-style\"><\/span><\/span><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-t80n3-af41b6c8b7dd23f9ba83a0e8567cb04b\">\n#top .av-special-heading.av-t80n3-af41b6c8b7dd23f9ba83a0e8567cb04b{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-t80n3-af41b6c8b7dd23f9ba83a0e8567cb04b .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-t80n3-af41b6c8b7dd23f9ba83a0e8567cb04b .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-t80n3-af41b6c8b7dd23f9ba83a0e8567cb04b av-special-heading-h4  avia-builder-el-13  el_after_av_hr  el_before_av_two_third '><h4 class='av-special-heading-tag '  itemprop=\"headline\"  >In che modo vengono coinvolti i muscoli <\/h4><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-12uefp-082b48559cac05bc5e9eb9ab13e4722c\">\n.flex_column.av-12uefp-082b48559cac05bc5e9eb9ab13e4722c{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-12uefp-082b48559cac05bc5e9eb9ab13e4722c av_two_third  avia-builder-el-14  el_after_av_heading  el_before_av_one_third  first flex_column_div av-zero-column-padding  '     ><section  class='av_textblock_section av-jtaakqqq-a58eae80025ad7ee1141924ec04b4fb8 '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><div class=\"page\" title=\"Page 19\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 21\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 21\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"page\" title=\"Page 28\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 28\">\n<div class=\"section\">\n<div class=\"page\" title=\"Page 12\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<p>I <strong>muscoli del cingolo pelvico<\/strong> sono i primi che vengono colpiti dal processo morboso.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Sempre pi\u00f9 evidente risulta la difficolt\u00e0 nel saltare, correre e nel salire le scale e presto l&#8217;impossibilit\u00e0 ad alzarsi da terra e da sedie basse.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Il paziente \u00e8 quindi costretto a camminare secondo il caratteristico pattern motorio caratterizzato da :<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<ul>\n<li>Iperlordosi lombare<\/li>\n<li>Flessione dell\u2019anca<\/li>\n<li>Estensione del ginocchio<\/li>\n<li>Abduzione con leggera intrarotazione dell&#8217;arto inferiore<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Equinismo del piede.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<\/ul>\n<p>Gradualmente la malattia si estende ai <strong>muscoli del cingolo superiore e della radice degli arti superiori<\/strong>:<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<ul>\n<li>Dentato, Pettorali, Gran Dorsale<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Bicipite brachiale, Brachioradiale<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Adduttori delle scapole<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<\/ul>\n<p>In un secondo tempo, solo qualche anno dopo, il processo si estende progressivamente ai <strong>muscoli del cingolo scapolare<\/strong>, e nelle fasi pi\u00f9 avanzate raggiunge i <strong>muscoli della faccia<\/strong>, risparmiando sempre la muscolatura estrinseca degli occhi, della mandibola, della lingua e delle corde vocali.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Infine i <strong>muscoli intercostali<\/strong> vanno incontro ad una lenta progressiva degenerazione Il diaframma resiste pi\u00fa a lungo.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Negli stadi terminali della malattia \u00e8 interessata anche la muscolatura distale degli arti.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div><\/section><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-yjeyl-91ff7cbc4e38eb219b6625a363606548\">\n.flex_column.av-yjeyl-91ff7cbc4e38eb219b6625a363606548{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-yjeyl-91ff7cbc4e38eb219b6625a363606548 av_one_third  avia-builder-el-16  el_after_av_two_third  el_before_av_hr  flex_column_div av-zero-column-padding  '     ><style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-juiuph3l-de3410522197f40d1d238d8cc70ea92a\">\n.avia-image-container.av-juiuph3l-de3410522197f40d1d238d8cc70ea92a img.avia_image{\nbox-shadow:none;\n}\n.avia-image-container.av-juiuph3l-de3410522197f40d1d238d8cc70ea92a .av-caption-image-overlay-bg{\nopacity:0.4;\nbackground-color:#000000;\n}\n.avia-image-container.av-juiuph3l-de3410522197f40d1d238d8cc70ea92a .av-image-caption-overlay-center{\ncolor:#ffffff;\n}\n<\/style>\n<div  class='avia-image-container av-juiuph3l-de3410522197f40d1d238d8cc70ea92a av-styling-no-styling av-hover-grow avia-align-center  avia-builder-el-17  avia-builder-el-no-sibling  noHover av-overlay-hover-deactivate'   itemprop=\"image\" itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/ImageObject\" ><div class=\"avia-image-container-inner\"><div class=\"avia-image-overlay-wrap\"><div class=\"av-image-caption-overlay\"><div class=\"av-caption-image-overlay-bg\"><\/div><div class=\"av-image-caption-overlay-position\"><div class=\"av-image-caption-overlay-center\"><\/div><\/div><\/div><img decoding=\"async\" fetchpriority=\"high\" class='wp-image-977 avia-img-lazy-loading-not-977 avia_image ' src=\"https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/distrofia-300x193.jpg\" alt='' title='muscolo atrofico'  height=\"193\" width=\"300\"  itemprop=\"thumbnailUrl\" srcset=\"https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/distrofia-300x193.jpg 300w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/distrofia-450x290.jpg 450w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/distrofia.jpg 700w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><\/div><\/div><\/div><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-jujggsc9-f7c0646a643cf0f5840d256cf3adf88a\">\n#top .hr.hr-invisible.av-jujggsc9-f7c0646a643cf0f5840d256cf3adf88a{\nheight:50px;\n}\n<\/style>\n<div  class='hr av-jujggsc9-f7c0646a643cf0f5840d256cf3adf88a hr-invisible  avia-builder-el-18  el_after_av_one_third  el_before_av_heading '><span class='hr-inner '><span class=\"hr-inner-style\"><\/span><\/span><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-n6czr-a559bd336f3c16781ddd072a54c495a9\">\n#top .av-special-heading.av-n6czr-a559bd336f3c16781ddd072a54c495a9{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-n6czr-a559bd336f3c16781ddd072a54c495a9 .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-n6czr-a559bd336f3c16781ddd072a54c495a9 .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-n6czr-a559bd336f3c16781ddd072a54c495a9 av-special-heading-h4  avia-builder-el-19  el_after_av_hr  el_before_av_one_full '><h4 class='av-special-heading-tag '  itemprop=\"headline\"  >La progressione della malattia<\/h4><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4\">\n.flex_column.av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4 av_one_full  avia-builder-el-20  el_after_av_heading  el_before_av_heading  first flex_column_div av-zero-column-padding  '     ><section  class='av_textblock_section av-jtaabdl7-515da227f3ed4c1f141e834a752c5dbc '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><div class=\"page\" title=\"Page 5\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 7\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<p><strong>La Distrofia Muscolare \u00e8 purtroppo, inesorabilmente progressiva<\/strong>; pu\u00f2 mostrare un miglioramento solo apparente della situazione clinica tra il 3\u00b0 &#8211; 4\u00b0 ed il 5\u00b0 &#8211; 8\u00b0 anno di et\u00e0, dovuto alla crescita muscolare fisiologica che sopravanza, mascherandola, la degenerazione.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<ul>\n<li>Fra gli 8 e i 9 anni si evidenzia generalmente l&#8217;impossibilit\u00e0 di salire le scale<\/li>\n<li>Fra i 9 e i 10 anni quella di alzarsi dalla sedia<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Fra i 9 e i 12 anni il bambino diviene incapace di camminare e viene progressivamente confinato in carrozzina.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<\/ul>\n<p>A dieci anni dall&#8217;esordio della malattia il paziente \u00e9 quasi sempre costretto in carrozzina o a letto.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Dopo i 20 anni di et\u00e0 trascorre a letto la maggior parte del suo tempo.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Il paziente muore purtroppo &nbsp;tra la seconda e la terza decade di vita, generalmente per complicanze cardio \u2013 respiratorie<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<div class=\"page\" title=\"Page 7\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 8\">\n<div class=\"layoutArea\">\n<div class=\"column\"><\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div><\/section><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-dxr87-cb10d125d20e6945750b58347aca4a07\">\n#top .av-special-heading.av-dxr87-cb10d125d20e6945750b58347aca4a07{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-dxr87-cb10d125d20e6945750b58347aca4a07 .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-dxr87-cb10d125d20e6945750b58347aca4a07 .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-dxr87-cb10d125d20e6945750b58347aca4a07 av-special-heading-h4  avia-builder-el-22  el_after_av_one_full  el_before_av_one_full '><h4 class='av-special-heading-tag '  itemprop=\"headline\"  >Come viene coinvolto il muscolo cardiaco<\/h4><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4\">\n.flex_column.av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-19y77s-6da3cf55bdcfb15d84d02fa3e68fadb4 av_one_full  avia-builder-el-23  el_after_av_heading  el_before_av_two_third  first flex_column_div av-zero-column-padding  '     ><section  class='av_textblock_section av-jtaabdl7-515da227f3ed4c1f141e834a752c5dbc '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><div class=\"page\" title=\"Page 5\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 7\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<p>Nella Distrofia Muscolare vi \u00e9 sempre un interessamento cardiaco sostenuto da un processo degenerativo che colpisce le fibre miocardiche analogamente a quanto avviene nel muscolo scheletrico, e che clinicamente si manifesta con:<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<ul>\n<li>Tachicardia<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Disturbi del ritmo<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<li>Cardiomegalia<span class=\"Apple-converted-space\">&nbsp;<\/span><\/li>\n<\/ul>\n<p>Viste le ridotte richiesta energetiche quasi mai sopraggiunge scompenso cardiaco tuttavia qualche volta la morte pu\u00f2 essere dovuta ad insufficienza cardiaca acuta.<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<p>Raramente il decesso, nella seconda o terza decade di vita, \u00e9 da attribuire ad arresto cardiaco<span class=\"Apple-converted-space\">&nbsp;<\/span><\/p>\n<div class=\"page\" title=\"Page 7\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<div class=\"page\" title=\"Page 8\">\n<div class=\"layoutArea\">\n<div class=\"column\"><\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<\/div><\/section><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-rrf0d-de73f17452d9f35340cdec6e6cef8212\">\n.flex_column.av-rrf0d-de73f17452d9f35340cdec6e6cef8212{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-rrf0d-de73f17452d9f35340cdec6e6cef8212 av_two_third  avia-builder-el-25  el_after_av_one_full  el_before_av_one_third  first flex_column_div av-zero-column-padding  column-top-margin'     ><p>\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-jiad3-bf6c4b81d5ce034cef421eca30aa5ae8\">\n#top .av-special-heading.av-jiad3-bf6c4b81d5ce034cef421eca30aa5ae8{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-jiad3-bf6c4b81d5ce034cef421eca30aa5ae8 .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-jiad3-bf6c4b81d5ce034cef421eca30aa5ae8 .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-jiad3-bf6c4b81d5ce034cef421eca30aa5ae8 av-special-heading-h4  avia-builder-el-26  el_before_av_textblock  avia-builder-el-first '><h4 class='av-special-heading-tag '  itemprop=\"headline\"  >TI interessa questo argomento dal punto di vista professionale?<\/h4><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div><br \/>\n<section  class='av_textblock_section av-jtaavp2p-b043e3bb1ee1fe883ec9bd3b03accd2a '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><p>Vorresti approfondire il tema della distrofia muscolare dal punto di vista dell&#8217;approccio terapeutico, dei trattamenti riabilitativi, della chinesiologia speciale e dell&#8217;approccio chirurgico?<\/p>\n<p>Potrebbe allora fare al caso tuo&nbsp;<a href=\"https:\/\/www.ikosecm.it\/la-distrofia-muscolare-di-duchenne-approccio-fisioterapico-riabilitativo.html\">questo corso ECM<\/a>&nbsp;distribuito da <a href=\"https:\/\/www.ikosecm.it\">IKOS ECM<\/a>&nbsp;dal titolo \u201c<a href=\"https:\/\/www.ikosecm.it\/la-distrofia-muscolare-di-duchenne-approccio-fisioterapico-riabilitativo.html\">La distrofia muscolare di Duchenne approccio fisioterapico riabilitativo<\/a>\u201d a cura del <em>Dott. Ivan Di Francescantonio<\/em>.<\/p>\n<p>Il corso prevede 4 capitoli e una prova di apprendimento che consiste in un questionario di valutazione finale a risposta multipla con 4 possibilit\u00e0 di risposta di cui una sola giusta. Sono previste&nbsp;30 domande.&nbsp; La soglia di superamento prevista \u00e8 del 75% con 5 tentativi possibili a disposizione.<\/p>\n<p>Dopo aver superato la prova finale, il corso dar\u00e0 diritto a 10 crediti ECM.<\/p>\n<\/div><\/section><br \/>\n<div  class='avia-button-wrap av-juymosjh-83e0566114ea9eed0e587fed90d7abfe-wrap avia-button-center  avia-builder-el-28  el_after_av_textblock  avia-builder-el-last '><a href='https:\/\/www.ikosecm.it\/la-distrofia-muscolare-di-duchenne-approccio-fisioterapico-riabilitativo.html'  class='avia-button av-juymosjh-83e0566114ea9eed0e587fed90d7abfe av-link-btn avia-icon_select-yes-right-icon avia-size-large avia-position-center avia-color-theme-color'   aria-label=\"Scopri di pi\u00f9\"><span class='avia_iconbox_title' >Scopri di pi\u00f9<\/span><span class='avia_button_icon avia_button_icon_right avia-iconfont avia-font-entypo-fontello' data-av_icon='\ue832' data-av_iconfont='entypo-fontello' ><\/span><\/a><\/div><\/p><\/div>\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-ju9mx8al-55ffa2aa3a5811753108342ce4e76fd8\">\n.flex_column.av-ju9mx8al-55ffa2aa3a5811753108342ce4e76fd8{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-ju9mx8al-55ffa2aa3a5811753108342ce4e76fd8 av_one_third  avia-builder-el-29  el_after_av_two_third  el_before_av_hr  flex_column_div av-animated-generic fade-in av-zero-column-padding avia-link-column av-column-link avia-link-column-hover  column-top-margin'    data-link-column-url=\"https:\/\/www.ikosecm.it\/app\/media\/uploads\/lezioni\/1933\/index.html\"  data-link-column-target=\"_blank\"   ><a class=\"av-screen-reader-only\" href=https:\/\/www.ikosecm.it\/app\/media\/uploads\/lezioni\/1933\/index.html  target=\"_blank\" >Segui un collegamento aggiunto manuale<\/a><p>\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-cyr73-58182adb61aaa07b0bbc1d221fcd6949\">\n#top .av-special-heading.av-cyr73-58182adb61aaa07b0bbc1d221fcd6949{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-cyr73-58182adb61aaa07b0bbc1d221fcd6949 .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-cyr73-58182adb61aaa07b0bbc1d221fcd6949 .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-cyr73-58182adb61aaa07b0bbc1d221fcd6949 av-special-heading-h3 blockquote classic-quote  avia-builder-el-30  el_before_av_image  avia-builder-el-first '><h3 class='av-special-heading-tag '  itemprop=\"headline\"  >Anteprima del corso<\/h3><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div><br \/>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-ju9mssb4-2db17a940efed9502da96dfc31856f6e\">\n.avia-image-container.av-ju9mssb4-2db17a940efed9502da96dfc31856f6e img.avia_image{\nbox-shadow:none;\n}\n.avia-image-container.av-ju9mssb4-2db17a940efed9502da96dfc31856f6e .av-image-caption-overlay-center{\ncolor:#ffffff;\n}\n<\/style>\n<div  class='avia-image-container av-ju9mssb4-2db17a940efed9502da96dfc31856f6e av-styling- av-hover-grow avia_animated_image av-animated-when-visible-95 left-to-right avia-align-center  avia-builder-el-31  el_after_av_heading  el_before_av_hr '   itemprop=\"image\" itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/ImageObject\" ><div class=\"avia-image-container-inner\"><div class=\"avia-image-overlay-wrap\"><img decoding=\"async\" fetchpriority=\"high\" class='wp-image-986 avia-img-lazy-loading-not-986 avia_image ' src=\"https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/screen-distrofia-300x176.jpeg\" alt='' title='screen distrofia'  height=\"176\" width=\"300\"  itemprop=\"thumbnailUrl\" srcset=\"https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/screen-distrofia-300x176.jpeg 300w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/screen-distrofia-768x450.jpeg 768w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/screen-distrofia-1030x604.jpeg 1030w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/screen-distrofia-705x413.jpeg 705w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/screen-distrofia-450x264.jpeg 450w, https:\/\/www.ikosecm.it\/ecm\/wp-content\/uploads\/2019\/05\/screen-distrofia.jpeg 1216w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><\/div><\/div><\/div><br \/>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-ju9svqe3-8cfd165acfd648d82f1c858e30ff1e0a\">\n#top .hr.hr-invisible.av-ju9svqe3-8cfd165acfd648d82f1c858e30ff1e0a{\nheight:30px;\n}\n<\/style>\n<div  class='hr av-ju9svqe3-8cfd165acfd648d82f1c858e30ff1e0a hr-invisible  avia-builder-el-32  el_after_av_image  el_before_av_animated_numbers '><span class='hr-inner '><span class=\"hr-inner-style\"><\/span><\/span><\/div><br \/>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-ju9n2o0t-59eade141083905d8b178c6bea5f469b\">\n#top .avia-animated-number.av-ju9n2o0t-59eade141083905d8b178c6bea5f469b.av-display-circle{\nmargin:40% 0 40% 0;\n}\n#top .avia-animated-number.av-ju9n2o0t-59eade141083905d8b178c6bea5f469b .avia-animated-number-title{\nfont-size:40px;\n}\n.avia-animated-number.av-ju9n2o0t-59eade141083905d8b178c6bea5f469b .avia-animated-number-circle{\nwidth:80%;\n}\n.avia-animated-number.av-ju9n2o0t-59eade141083905d8b178c6bea5f469b .avia-animated-number-circle-inner{\nborder-style:none;\nbox-shadow:none;\n}\n<\/style>\n<div  class=\"avia-animated-number av-ju9n2o0t-59eade141083905d8b178c6bea5f469b av-force-default-color avia_animate_when_visible  avia-builder-el-33  el_after_av_hr  avia-builder-el-last  av-display-circle \" data-timer=\"3000\"><span class='avia-animated-number-circle '><span class='avia-animated-number-circle-inner'><\/span><\/span><strong class=\"heading avia-animated-number-title\"><span class=\"avia-single-number __av-single-number\" data-number_format=\"\" data-number=\"10\" data-start_from=\"0\">10<\/span><\/strong><div class=\"avia-animated-number-content\"><p>Crediti ECM<\/p>\n<\/div><\/div><\/p><\/div><\/p>\n<div  class='hr av-d0lho-f9b6919b96a7ea17baea2d49a5ce7ebb hr-default  avia-builder-el-34  el_after_av_one_third  el_before_av_heading '><span class='hr-inner '><span class=\"hr-inner-style\"><\/span><\/span><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-9tlw7-6d2a18a5f3bbc7e61f6fcf1e8eabb3a5\">\n#top .av-special-heading.av-9tlw7-6d2a18a5f3bbc7e61f6fcf1e8eabb3a5{\npadding-bottom:10px;\n}\nbody .av-special-heading.av-9tlw7-6d2a18a5f3bbc7e61f6fcf1e8eabb3a5 .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-9tlw7-6d2a18a5f3bbc7e61f6fcf1e8eabb3a5 .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-9tlw7-6d2a18a5f3bbc7e61f6fcf1e8eabb3a5 av-special-heading-h4  avia-builder-el-35  el_after_av_hr  el_before_av_two_third '><h4 class='av-special-heading-tag '  itemprop=\"headline\"  >Che bello sarebbe poter avere accesso  a tutti i corsi IKOS ECM&#8230;<\/h4><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-eqi5r-167342179bfa5bb25feac7d146468f0b\">\n.flex_column.av-eqi5r-167342179bfa5bb25feac7d146468f0b{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-eqi5r-167342179bfa5bb25feac7d146468f0b av_two_third  avia-builder-el-36  el_after_av_heading  el_before_av_one_third  first flex_column_div av-zero-column-padding  '     ><p><section  class='av_textblock_section av-jsx3alm2-6954c7b7fce382362b4c0e25114eaf7b '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/BlogPosting\" itemprop=\"blogPost\" ><div class='avia_textblock'  itemprop=\"text\" ><p>&#8230;con la &nbsp;<strong>GLOBAL CARD<\/strong>&nbsp;\u00e8 possibile!<\/p>\n<p>Con un&#8217;unica spesa di soli <strong>\u20ac 199,00<\/strong> (esente iva) potrai accedere <strong>a tutti i corsi ECM FAD<\/strong> presenti nel catalogo IKOS oppure, qualora ti servisse,&nbsp;trasferire i crediti al triennio precedente seguendo <a href=\"https:\/\/www.ikosecm.it\/ecm\/la-normativa-ecm\/cogeaps-come-trasferire-i-crediti-ecm-del-triennio-precedente\/\">questa semplice procedura<\/a>.<\/p>\n<\/div><\/section><br \/>\n<div  class='avia-button-wrap av-jsx3bseu-13205b2e28bd7025b71aec05e4e5e569-wrap avia-button-left  avia-builder-el-38  el_after_av_textblock  avia-builder-el-last '><a href='https:\/\/www.ikosecm.it\/global-card.php'  class='avia-button av-jsx3bseu-13205b2e28bd7025b71aec05e4e5e569 av-link-btn avia-icon_select-no avia-size-large avia-position-left avia-color-theme-color'  target=\"_blank\"  rel=\"noopener noreferrer\"  aria-label=\"Scopri la Global Card\"><span class='avia_iconbox_title' >Scopri la Global Card<\/span><\/a><\/div><\/p><\/div>\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-72t07-0e3e037d189a05633ea8026437435514\">\n.flex_column.av-72t07-0e3e037d189a05633ea8026437435514{\nborder-radius:0px 0px 0px 0px;\npadding:0px 0px 0px 0px;\n}\n<\/style>\n<div  class='flex_column av-72t07-0e3e037d189a05633ea8026437435514 av_one_third  avia-builder-el-39  el_after_av_two_third  el_before_av_hr  flex_column_div av-zero-column-padding  '     ><p>\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-jsx2nve0-a7ee6861869ce6f15a81a6e3919d382b\">\n.avia-image-container.av-jsx2nve0-a7ee6861869ce6f15a81a6e3919d382b img.avia_image{\nbox-shadow:none;\n}\n.avia-image-container.av-jsx2nve0-a7ee6861869ce6f15a81a6e3919d382b 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distrofina.<\/p>\n","protected":false},"author":5,"featured_media":2961,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[25,24],"tags":[129,89,59,124,125,123,128,117,66,91,257,130,126,127],"class_list":["post-943","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-corsi-ecm","category-in-evidenza","tag-andatura-anserina","tag-corsi-ecm","tag-corso-ecm","tag-corso-ecm-distrofia","tag-distrofia-duchenne","tag-distrofia-muscolare","tag-distrofinopatie","tag-dolore-spalla","tag-ecm","tag-ecm-fad","tag-f-a-d","tag-ipertrofia-dei-cingoli","tag-malattia-degenerativa","tag-malattia-progressiva"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v25.5 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>La Distrofia Muscolare di Duchenne , speciale per gli addetti ai lavori<\/title>\n<meta name=\"description\" content=\"la distrofia muscolare 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